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Beckwith-Wiedemann syndrome constitutes a clinicopathologic entity characterized macroglossia,
omphalocele or umblical hernia, visceromegaly, postnatal gigantism, microcephaly, Nevus flammeus,
ear lobe grooves, hemihypertrophy and other abnormalities.
The anomalies of the syndrome are facultative and not obligatory.
We experience one case of Beck with-Wiedemann syndrome. This 1-day-aged female neonate
showed macroglossia, gigantism, omphalocele and hypoglycemia.
Review of literature was done briefly.
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